Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome

نویسندگان

  • Ricardo Alicea-Guevara
  • Michael Cruz Caliz
  • Jose Adorno
  • Ricardo Fernandez
  • Kelvin Rivera
  • Gustavo Gonzalez
  • Ricardo Alan Hernandez-Castillo
  • Rosangela Fernandez
  • Christian Castillo Latorre
چکیده

Hereditary haemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding.

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عنوان ژورنال:

دوره 2018  شماره 

صفحات  -

تاریخ انتشار 2018